Abstract

GUARNIERI, Caroline Ló; PATUZZI, Eduarda; JARDIM, Juliana Jobim  and  SILVA, Berenice Barbachan e. Dental management of Rendu-Osler-Weber Syndrome: case report. Rev. Assoc. Paul. Cir. Dent. [online]. 2016, vol.70, n.3, pp. 256-259. ISSN 0004-5276.

The Rendu-Osler-Weber Syndrome or Hereditary Hemorrhagic Telangiectasia (HHT) is a rare systemic fibrovascular dysplasia, which causes a defect in the elastic and muscle layer of the blood vessel wall, turning them more vulnerable to traumas and spontaneous ruptures. The dentists can play an important role in this diagnostic because the first signs often appear in the mouth, such as telangiectasia and recurrent bleeding in the oral mucosa. The management of this patient should be appropriate to its systemic profile to ensure the safety and effectiveness of dental treatment. This work aims to describe the main characteristics of this syndrome, its peculiarities and limitations of management during dental treatment, followed by the presentation of a clinical case.

Keywords : telangiectasia; hereditary hemorrhagic; arteriovenous malformations; epistaxis; oral health; practice patterns; dentists..