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Brazilian Journal of Oral Sciences

versão On-line ISSN 1677-3225

Resumo

BOMFIN, Luana Eschholz et al. Keratocystic odontogenic tumor related to nevoid basal cell carcinoma syndrome: clinicopathological study. Braz. J. Oral Sci. [online]. 2013, vol.12, n.1, pp. 23-29. ISSN 1677-3225.

AIM: To assess clinicopathological features of patients with keratocystic odontogenic tumor (KCOT) associated with nevoid basal cell carcinoma syndrome (NBCCS) in a single Brazilian institution. METHODS: After histopathological analyses of KCOT related to NBCCS, the medical charts of 14 patients were assessed. These patients presented a total of 31 primary and 8 recurrent KCOT. RESULTS: Out of 14 patients, 8 presented a single KCOT, 4 showed synchronous tumors, 1 had 3 metachronous lesions and another patient had 2 synchronous lesions at initial evaluation and then developed other 3 metachronous lesions. Besides the 31 primary KCOTs, 18 lesions were located in mandible and 13 in maxilla. Most tumors presented unilocular pattern and association with a tooth. CONCLUSIONS: KCOT is a frequent manifestation of NBCCS and can be its first sign, mainly in young patients. In contrast to a previously published series, most patients presented a single lesion.

Palavras-chave : Gorlin syndrome; keratocyst; keratocystic odontogenic tumor; nevoid basal cell carcinoma syndrome.

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