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Revista de Cirurgia e Traumatologia Buco-maxilo-facial

  ISSN 1808-5210

PRADO, Bruno Nifossi et al. Parry Romberg Syndrome. Rev. cir. traumatol. buco-maxilo-fac. []. 2012, 12, 2, pp. 09-12. ISSN 1808-5210.

The Parry-Romberg syndrome, or progressive facial hemiatrophy, was first described by Parry in 1825 and Romberg in 1846. It is a disease of unknown origin1 that usually develops in the first or second decade of life2. Females are more affected than males in a ratio of 1.5:1.0. It is rarely found bilaterally3, affecting only one hemiface in 95% of cases. The aim of this study was to elucidate a clinical case difficult to diagnose of a rare syndrome with no definitive treatment, only aesthetic. The 39-year-old female patient had developed a white spot on the left side seven years earlier that migrated onto the rest of her face. For approximately the past one and half years it has progressed as a mild facial atrophy involving skin and muscle in the left zygomatic maxillary region. The Parry-Romberg syndrome is a rare disease of slow progression that affects the tissues of the face, being difficult to diagnose and lacking any definitive treatment.

: Syndrome; Facial Hemiatrophy; atrophy.

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