Prosthetic rehabilitation for a patient with hypohidrotic ectodermal dysplasia: a clinical case

Guna Shekhar^I; Alluri RamaRaju^II; Chandrasekhar Rao^III; Sarada^I

^IAssociate Professor, Faculty of Pediatric Dentistry, VDC, NTR University of Health Sciences, AP, India
^IIProfessor, Faculty of Prosthetic Dentistry, VDC, NTR University of Health Sciences, AP, India
^IIIProfessor, Faculty of Pediatric Dentistry, VDC, NTR University of Health Sciences, AP, India

Correspondence

ABSTRACT

Hypohidrotic ectodermal dysplasia (HED) is a hereditary syndrome, characterized by a classic triad of hypotrichosis, hypodontia and hypohidrosis. The case of an 8-year-old girl with HED presenting oligodontia and marked resorption of maxillary and mandibular alveolar ridges is reported. A specially designed aluminum wire tray was used for taking impressions of both dental arches. Prosthetic rehabilitation included a removable maxillary overdenture and a mandibular conventional acrylic resin denture made tissue-compatible by means of a soft denture liner attached to denture base. The proposed treatment plan provided improved esthetics, function, and quality of life.

Keywords: ectodermal dysplasia, oligodontia, soft liner, mucosa supported dentures.

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Correspondence to:
Guna Shekhar
c/o M.Prakash, 160, 5th Cross,
28th main, sector-1, HSR Layout,
Bangalore-102, INDIA ]]> E-mail: drguna1234@yahoo.com

Received for publication: December 04, 2009
Accepted: March 04, 2010