Abstract

STOLZ, Alexsandra da Silva Botezeli; OLIVEIRA, Marcia Oliva de; FERREIRA, Fabiana Vargas  and  UGGERI, Celina Maria. Follow-up of patient with Gorlin-Goltz Syndrome - a case report. RSBO (Online) [online]. 2010, vol.7, n.2, pp.226-230. ISSN 1984-5685.

INTRODUCTION: The Gorlin-Goltz Syndrome, also known as Nevoid Basal Cell Carcinoma Syndrome, is a dominant autosomal hereditary disorder which is characterized by the presence of multiple jaw keratocysts and basal cell carcinomas, besides musculoskeletal, neurological, dermatological and endocrine abnormalities. CASE REPORT: This paper reports the case of a fifteen-year-old patient who was referred to the Faculty of Dentistry of the Federal University of Santa Maria (RS, Brazil) and presented multiple jaw keratocysts, which were surgically removed in several steps. The patient is under observation for 48 months, including clinical and radiographic evaluations. CONCLUSION: It can be concluded that systematic and regular monitoring may avoid possible harmful consequences to the patient.

Keywords : Gorlin-Goltz Syndrome; basal cell carcinoma; odontogenic cysts.

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