Abstract

SANTOS, Rennan Luiz Oliveira dos et al. Surgical approach in patient with dysostosis cleidocranial. Rev. cir. traumatol. buco-maxilo-fac. [online]. 2016, vol.16, n.3, pp. 40-43. ISSN 1808-5210.

The Cleidocranial dysostosis (CCD) was described and conceptualized for the first time in 1897 by Marie and Sainton. The pattern of in heritance is autosomal dominant but, in some cases, externalinterference in the fetal period could cause genetic mutation preventing the transformation of mesenchymal stem cells into osteoblasts. This pathologyis characterized by cranial malformations, abnormalities of the clavicles, supernumerary teeth and dental retentions. Radiologicalstudies are extremelyimportanttoa precise diagnosis. Thisstudy aims to present a dental surgicaltreatment in patientswiththispathology.

Keywords : Congenital deformity; Cleidocranial dysostosis..